Sarcoidosis of the orbit: a rare clinical case and literature review

Authors

  • A. Cekov Neurosurgery Clinic, University Hospital “Acibadem City Clinic Tokuda - EAD”, Sofia, Bulgaria Author
  • A. Kanev Neurosurgery Clinic, University Hospital “Acibadem City Clinic Tokuda - EAD”, Sofia, Bulgaria Author

DOI:

https://doi.org/10.2478/amb-2024-0043

Keywords:

isolated sarcoidosis, orbital tumour, exophthalmos

Abstract

Sarcoidosis is a systemic disease of still-unknown etiology in which characteristic granulomas develop in various parts of the body. Symptoms depend on the localization of the formations. The isolated orbital form, in which granulomas develop only in the orbit of 
the eye, is very rare and presents a challenge in terms of differential diagnosis. Treatment for the orbital form may include a conservative, surgical, or combined approach. The goal of surgical treatment is to completely remove the tumour formation, which achieves excellent results in many cases. The current article presents a clinical case of an isolated orbital form of sarcoidosis, in which surgical treatment was undertaken with complete removal of the granulomatous formation. In the postoperative follow-up, a complete reversal of the symptoms was observed without residual disturbances in vision or eye movements.

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Published

10.09.2024

How to Cite

Cekov, A., & Kanev, A. (2024). Sarcoidosis of the orbit: a rare clinical case and literature review. Acta Medica Bulgarica, 51(3), 58-62. https://doi.org/10.2478/amb-2024-0043